It is also called autoimmune pancreatitis, sclerosing pancreatitis, nonalcoholic destructive pancreatitis. HISORt diagnostic criteria developed by Mayo Clinic are used in diagnosis.
Although glucocorticoids are used in the treatment (recommended dose: starting prednisone 40 mg/day and stopping the treatment after 4-6 weeks by 5 mg per week), the optimal dose and duration are still unknown.
Autoimmune pancreatitis is a form of chronic pancreatitis with distinctive clinical, histological and morphological features that develops due to autoimmune etiology.
This form of chronic pancreatitis was first described by Sarles et al. in 1961, and the term autoimmune pancreatitis was first used by Yoshida et al. in 1995. In 2003, Kamisawa et al. reported that autoimmune pancreatitis is a systemic disease, and the presence of IgG4-positively stained plasma cells in the pancreas and other affected organs (4).
Although the first reported cases in the literature were from Japan, the incidence is increasing all over the world with the increase in detectability. Autoimmune pancreatitis; It may occur as a primary pancreatic disease or may progress with other autoimmune diseases (eg primary sclerosing cholangitis, primary biliary cirrhosis, retroperitoneal fibrosis, rheumatoid arthritis, sarcoidosis, Sjögren’s syndrome).